ALDH3A2
aldehyde dehydrogenase 3 family member A2
- Ensembl:
- ENSG00000072210
- UniProt:
- P51648
- OMIM:
- 609523
- Synonyms:
- ALDH10, FALDH, SLS
Cilia effects upon perturbation of ALDH3A2
Ciliogenesis screen results (5 screens)
- Kim2016: Not Reported
- Wheway et al. 2015 (siRNA) [siRNA]: No effect PMID:26167766
- Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
- Roosing et al. 2015 (siRNA) [siRNA]: No effect PMID:26595381
- Kim et al. 2010 (siRNA) [siRNA]: Shorter Cilia (Area per Cilia z=-3.14) PMID:20393562
Phenotypes
- Mouse phenotype:
- decreased circulating alkaline phosphatase level; abnormal behavior; increased startle reflex; decreased prepulse inhibition; decreased locomotor activity
Ciliopathy associations
- Sjögren-Larsson Syndrome
Subcellular localization
cilia associated gene, cytosol, endoplasmic reticulum
Function
Sjögren-Larsson syndrome is caused by a mutation in the ALDH3A2 gene, which produces fatty aldehyde dehydrogenase (FALDH). FALDH is a membrane-bound protein involved in fatty oxidation. Structural disturbance and poor metabolite clearance likely contribute to pathogenesis(PMID: 40736838).