ANKS6

ankyrin repeat and sterile alpha motif domain containing 6

Ensembl:
ENSG00000165138
UniProt:
Q68DC2
OMIM:
615370
Synonyms:
ANKRD14, FLJ36928, NPHP16, SAMD6

Cilia effects upon perturbation of ANKS6

Loss-of-function effect:
Shorter cilia

Ciliogenesis screen results (3 screens)

  • Wheway et al. 2015 (siRNA) [siRNA]: No effect PMID:26167766
  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
  • Pusapati et al. 2018 (CRISPR) [CRISPR]: Positive Regulator (Hh signaling, neg_rank=761, lfc=-0.52) PMID:30270045

Phenotypes

Mouse phenotype:
preweaning lethality, complete penetrance
Human ciliopathy phenotype:
nephronophthisis 16

Ciliopathy associations

  • Nephronophthisis
  • Polycystic Kidney Disease

Subcellular localization

cilia

Functional category

  • Ciliary assembly/disassembly

Function

Ciliopathy gene NPHP16. Found in Inv compartment of cilia, where it undergoes phosphorylation (29395339).