ARL2

ARF like GTPase 2

Ensembl:
ENSG00000213465
UniProt:
P36404
OMIM:
601175
Synonyms:
ARFL2

Cilia effects upon perturbation of ARL2

Cilia number / % ciliated:
Decreased cilia number
Loss-of-function effect:
Shorter cilia
Overexpression effect:
Shorter cilia

Ciliogenesis screen results (4 screens)

  • Kim2016: No effect
  • Wheway et al. 2015 (siRNA) [siRNA]: No effect PMID:26167766
  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
  • Roosing et al. 2015 (siRNA) [siRNA]: No effect PMID:26595381

Ciliopathy associations

  • Retinal Dystrophy/Degeneration

Subcellular localization

centrosome, cilia, mitochondria, nucleus

Functional category

  • Ciliary assembly/disassembly
  • Trafficking (BBSome, small GTPases, vesicular transport, ATPases)
  • Actin & cytoskeleton regulation
  • Metabolism
  • Protein processing & maturation
  • Cell migration & adhesion
  • Signaling (Hedgehog, GPCRs, ion channels)

Function

Regulates cilia stability and development of outer segments in rod photoreceptor neurons(30446707).

Model organism evidence

Mus musculus (3 references)

To evaluate this function in the retina, we conditionally deleted ARL2 in mouse retina at two distinct stages, either during the embryonic development (retArl2-/-) or after ciliogenesis specifically in rods (rodArl2-/-).

Roles for ELMOD2 and Rootletin in ciliogenesis.

PMIDs: 36611941, 33596093, 30446707