CFAP221

cilia and flagella associated protein 221

Ensembl:
ENSG00000163075
UniProt:
Q4G0U5
OMIM:
618704
Synonyms:
FAP221, PCDP1

Cilia effects upon perturbation of CFAP221

Ciliogenesis screen results (1 screen)

  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680

Ciliopathy associations

  • Primary Ciliary Dyskinesia

Subcellular localization

cilia

Functional category

  • Ciliary assembly/disassembly
  • Actin & cytoskeleton regulation
  • T cell biology
  • Reproduction & sperm
  • Cell migration & adhesion

Function

Mouse homologue Pcdp1 causes PCD and brain defects in mice when mutated (18039845, 25073043). Interacts with CFAP54 and SPEF2 (32704025). Identified as a cause of PCD in humans in 2020 (31636325)

Model organism evidence

Mus musculus (2 references)

Airway ciliary microenvironment responses in mice with primary ciliary dyskinesia and central pair apparatus defects.

Genetic interaction between central pair apparatus genes CFAP221, CFAP54, and SPEF2 in mouse models of primary ciliary dyskinesia.

PMIDs: 39558053, 32704025