MUC5AC

mucin 5AC, oligomeric mucus/gel-forming

Ensembl:
ENSG00000291363, ENSG00000215182
UniProt:
P98088
OMIM:
158373
Synonyms:
MUC5

Cilia effects upon perturbation of MUC5AC

Cilia number / % ciliated:
Incrased cilia number

Ciliogenesis screen results (2 screens)

  • Wheway et al. 2015 (siRNA) [siRNA]: Ciliogenesis Defect (z=-3.29) PMID:26167766
  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680

Phenotypes

Mouse phenotype:
abnormal skin coloration, preweaning lethality, incomplete penetrance
Mouse ciliopathy phenotype:
persistence of hyaloid vascular system

Subcellular localization

cilia associated gene

Functional category

  • Ciliary assembly/disassembly
  • Signaling (Hedgehog, GPCRs, ion channels)

Function

MUC5B mobilizes and MUC5AC spatially aligns mucociliary transport on human airway epithelium ( 36427316)

Model organism evidence

Mus musculus (1 reference)

The SIRT3-KO group displayed reduced cilia length.

PMIDs: 41311539