PIEZO1

piezo type mechanosensitive ion channel component 1 (Er blood group)

Ensembl:
ENSG00000103335
UniProt:
Q92508
OMIM:
611184
Synonyms:
FAM38A, KIAA0233

Cilia effects upon perturbation of PIEZO1

Loss-of-function effect:
Shorter cilia
Overexpression effect:
Increased

Ciliogenesis screen results (2 screens)

  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
  • Elliott et al. 2025 (CRISPRa) [CRISPRa]: Disassembly Trigger (casTLE Effect=-2.89) PMID:41160700

Phenotypes

Mouse phenotype:
decreased locomotor activity, abnormal limb bud morphology, preweaning lethality, complete penetrance, abnormal embryo size, pallor, abnormal placenta size, pale yolk sac, embryonic growth retardation
Mouse ciliopathy phenotype:
increased circulating alanine transamise level, abnormal uriry bladder morphology

Subcellular localization

cilia

Functional category

  • Ciliary assembly/disassembly
  • Actin & cytoskeleton regulation
  • Cell migration & adhesion
  • Signaling (Hedgehog, GPCRs, ion channels)
  • Cardiac & muscle development

Function

Piezo1 co-localized with primary cilia in mandibular condyle chondrocytes (35279604).

Model organism evidence

Mus musculus (1 reference)

PIEZO1-Primary Cilia Axis Mediates Compressive Stress-Induced Growth Plate Degeneration and Ossification in Adolescent Idiopathic Scoliosis.

PMIDs: 41194970