PTPN11
protein tyrosine phosphatase non-receptor type 11
- Ensembl:
- ENSG00000179295
- UniProt:
- Q06124
- OMIM:
- 176876
- Synonyms:
- BPTP3, NS1, PTP2C, SH-PTP2, SHP-2
Cilia effects upon perturbation of PTPN11
- Cilia number / % ciliated:
- Decreased cilia number
- Loss-of-function effect:
- Shorter cilia
Ciliogenesis screen results (5 screens)
- Kim2016: Not Reported
- Wheway et al. 2015 (siRNA) [siRNA]: Ciliogenesis Defect (z=-2.09) PMID:26167766
- Breslow et al. 2018 (CRISPR) [CRISPR]: Increased Signaling (Negative Regulator) PMID:29459680
- Roosing et al. 2015 (siRNA) [siRNA]: No effect PMID:26595381
- Elliott et al. 2025 (CRISPRa) [CRISPRa]: Disassembly Trigger (casTLE Effect=-3.88) PMID:41160700
Subcellular localization
cilia, cytosol, nucleus
Functional category
- Ciliary assembly/disassembly
- Actin & cytoskeleton regulation
- T cell biology
- Viral interactions
- Cell migration & adhesion
- Signaling (Hedgehog, GPCRs, ion channels)
- ECM & connective tissue
- Transcription regulation
Function
Also called SHP2. Responsible for craniofacial skeletal formation by regulation of primary cilia formation in chondrocytes, especially in the craniofacial region. Positively regulates ciliogenesis through IFT regulation in condyle cartilage. Deficiency shortens length and reduces number of primary cilia (25919282).