SEPTIN8

septin 8

Ensembl:
ENSG00000164402
UniProt:
Q92599
OMIM:
608418
Synonyms:
KIAA0202, SEP2, SEPT8, SEPTIN-8

Cilia effects upon perturbation of SEPTIN8

Loss-of-function effect:
Longer cilia

Phenotypes

Mouse phenotype:
decreased prepulse inhibition, decreased mean corpuscular volume, abnormal startle reflex, increased startle reflex, abnormal locomotor activation, decreased bone mineral density, increased circulating phosphate level

Subcellular localization

basal body, transition zone

Functional category

  • Ciliary assembly/disassembly
  • Trafficking (BBSome, small GTPases, vesicular transport, ATPases)
  • Actin & cytoskeleton regulation
  • Transition zone

Function

Septins are either enriched at the apical cell cortex including the ciliary bases (septin-2, -4, -6, and -7), or show axonemal staining (septin-2, -7, -9 and -11) or specifically localize to ciliary sub-compartments (septin-8 and -9)(24317785).

Model organism evidence

C. elegans (1 reference)

Primary cilia rely on compartmentalisation mechanisms that establish the organelle's protein and lipid composition.

PMIDs: 41279625