SNAP23

synaptosome associated protein 23

Ensembl:
ENSG00000092531
UniProt:
O00161
OMIM:
602534
Synonyms:
HST17016, SNAP23A, SNAP23B

Cilia effects upon perturbation of SNAP23

Ciliogenesis screen results (3 screens)

  • Wheway et al. 2015 (siRNA) [siRNA]: Ciliogenesis Defect (z=-4.65) PMID:26167766
  • Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
  • Roosing et al. 2015 (siRNA) [siRNA]: No effect PMID:26595381

Phenotypes

Mouse phenotype:
embryonic lethality prior to organogenesis, increased startle reflex, preweaning lethality, complete penetrance, abnormal coat/hair pigmentation

Subcellular localization

cilia, nucleus

Functional category

  • Ciliary assembly/disassembly
  • Trafficking (BBSome, small GTPases, vesicular transport, ATPases)
  • Actin & cytoskeleton regulation
  • T cell biology

Function

S P23 has localized in primary cilia.

Model organism evidence

Mus musculus (2 references)

Nephrocystin (NPHP1) is a ciliary transition zone protein and its ablation causes nephronophthisis (NPHP) with partially penetrant retinal dystrophy.

Mutations in the centrosomal protein 290 (CEP290) gene cause various ciliopathies involving retinal degeneration.

PMIDs: 33961633, 31694913