TTC6
tetratricopeptide repeat domain 6
- Ensembl:
- ENSG00000139865
- UniProt:
- Q86TZ1
- OMIM:
- 620954
- Synonyms:
- C14ORF25, NCRNA00291
Cilia effects upon perturbation of TTC6
- Cilia number / % ciliated:
- Decreased cilia number
- Loss-of-function effect:
- Shorter cilia
Ciliogenesis screen results (4 screens)
- Kim2016: Not Reported
- Breslow et al. 2018 (CRISPR) [CRISPR]: No Significant Effect PMID:29459680
- Roosing et al. 2015 (siRNA) [siRNA]: No effect PMID:26595381
- Kim et al. 2010 (siRNA) [siRNA]: Longer Cilia (Area per Cilia z=2.38) PMID:20393562
Subcellular localization
basal body, cilia
Functional category
- Ciliary assembly/disassembly
Function
Mutated in MKS. TTC6 localizes to the centrosome and ciliary shaft in controls but only to the centrosome in patient fibroblasts (32055034)